Search results for "KAWASAKI DISEASE"

showing 10 items of 41 documents

Coronavirus disease 2019, Kawasaki disease, and multisystem inflammatory syndrome in children

2020

2019-20 coronavirus outbreakDelayed DiagnosisCoronavirus disease 2019 (COVID-19)Pneumonia ViralMucocutaneous Lymph Node Syndromemedicine.disease_causeDelayed diagnosisArticleBetacoronavirusPandemicmedicineHumansPediatrics Perinatology and Child HealthChildLetter to the EditorPandemicsCoronavirusbiologybusiness.industrySARS-CoV-2COVID-19biology.organism_classificationmedicine.diseaseVirologyMucocutaneous Lymph Node SyndromeCoronavirusPediatrics Perinatology and Child HealthKawasaki diseasebusinessCoronavirus InfectionsBetacoronavirusThe Journal of Pediatrics
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Kawasaki disease epidemic: pitfalls

2020

AbstractRecent reports have described in the pediatric population a new type of hyperinflammatory response manifested following contact with SARS-CoV-2, with some of the clinical features attributable to Kawasaki disease (KD). The purpose of this commentary is to remark on a possible recent association between SARS-CoV-2 and KD. Although today little is known about the etiology of KD, the most accepted hypothesis is that of a probable viral etiology, therefore, even the SARS-CoV-2 virus could trigger, in genetically predisposed subjects, an exaggerated inflammatory response that is clinically evident like the one described in KD.

2019-20 coronavirus outbreakSevere acute respiratory syndrome coronavirus 2 (SARS-CoV-2)Inflammatory responsevirusesPneumonia ViralHyperinflammatory response; Kawasaki disease; Pediatric population; SARS-CoV-2; COVID-19; Coronavirus Infections; Humans; Mucocutaneous Lymph Node Syndrome; Pandemics; Pneumonia Viral; SARS-CoV-2; BetacoronavirusMucocutaneous Lymph Node SyndromeVirusBetacoronavirusSettore MED/38 - Pediatria Generale E SpecialisticaMedicineHumansPediatric populationViralskin and connective tissue diseasesPandemicsViral etiologyKawasaki diseasebusiness.industrySARS-CoV-2lcsh:RJ1-570COVID-19lcsh:PediatricsPneumoniamedicine.diseaseHyperinflammatory responseImmunologyEtiologyCommentaryKawasaki diseasebusinessCoronavirus InfectionsPediatric populationItalian Journal of Pediatrics
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Revascularisation of a Giant Coronary Artery Aneurysm in Suspected Incomplete Kawasaki-Disease

2006

Kawasaki disease leads to typical vascular complications in up to 20 % of untreated cases. We describe a 47-year-old patient with coronary vessel disease, involving the right coronary artery with a huge aneurysmatic dilatation, suspicious for an incomplete form of Kawasaki disease. We found little information about the surgical treatment and postoperative course of this disease in adults. Typically, these infrequent patients present with acute myocardial infarction and require interdisciplinary decision-making.

Brain InfarctionPulmonary and Respiratory Medicinemedicine.medical_specialtyMyocardial InfarctionDiseaseMucocutaneous Lymph Node SyndromeCoronary AngiographyPostoperative ComplicationsAneurysmInternal medicinemedicine.arterymedicineHumanscardiovascular diseasesMyocardial infarctionCoronary Artery BypassSurgical treatmentCoronary artery aneurysmbusiness.industryCoronary ThrombosisCoronary AneurysmMiddle Agedmedicine.diseaseAortic DissectionIntracranial EmbolismRight coronary arteryCoronary vesselCardiologySurgeryKawasaki diseaseCardiology and Cardiovascular MedicinebusinessThe Thoracic and Cardiovascular Surgeon
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COVID-19 and relapsing Kawasaki disease: a case report during the pandemia

2020

Introduction: The pandemia of COVID-19 remains a global health alarm with high incidence of lethality, especially in older age groups who suffer from underlying medical conditions. However, children are less likely to manifest severe conditions. Objectives: COVID-19 was correlated to a higher incidence and a suspected increased risk of Kawasaki Disease (KD) in children.

COVID-19Kawasaki Disease
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COVID-19 temporally related multisystem inflammatory syndrome (MIS-C): an early window of opportunity is a good treatment strategy? The experience of…

2021

Introduction: Multi-system inflammatory syndrome in children (MISC) shows a presentation mimicking Kawasaki Disease (KD), Toxic Shock Syndrome (TSS), Macrophage Activation Syndrome (MAS). Furthermore, many children show respiratory or abdominal symptoms. Objectives: Intravenous immunoglobulin (IVIG) is recommended as first line treatment as in KD, followed by aspirin, steroids and, in IVIGresistant patients, IL-1 or IL-6 blocking agents. Methods: We describe a cohort of 16 Sicilian children (6M;10F; age:1.4-14 years), with MIS-C, with clinical features compatible with classical or incomplete KD, in some cases with MAS and/or TSS. Demographic, clinical, laboratory, echocardiographic and imag…

COVID-19MIS-CKawasaki DiseaseSettore MED/38 - Pediatria Generale E Specialistica
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Increased percentages of tumor necrosis factor-alpha+/interferon-gamma+ T lymphocytes and calprotectin+/tumor necrosis factor-alpha+ monocytes in pat…

2012

CalprotectinSettore MED/38 - Pediatria Generale E SpecialisticaKawasaki Disease; Calprotectin; TNF alfaKawasaki DiseaseTNF alfa
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Defining Kawasaki disease and pediatric inflammatory multisystem syndrome-temporally associated to SARS-CoV-2 infection during SARS-CoV-2 epidemic in…

2021

Abstract Background There is mounting evidence on the existence of a Pediatric Inflammatory Multisystem Syndrome-temporally associated to SARS-CoV-2 infection (PIMS-TS), sharing similarities with Kawasaki Disease (KD). The main outcome of the study were to better characterize the clinical features and the treatment response of PIMS-TS and to explore its relationship with KD determining whether KD and PIMS are two distinct entities. Methods The Rheumatology Study Group of the Italian Pediatric Society launched a survey to enroll patients diagnosed with KD (Kawasaki Disease Group – KDG) or KD-like (Kawacovid Group - KCG) disease between February 1st 2020, and May 31st 2020. Demographic, clini…

Coronary artery abnormalities; Hypotension; Kawasaki disease; Multisystem inflammatory syndrome associated with coronavirus disease; Myocarditis; Pediatric inflammatory multisystem syndrome-temporally associated to SARS-CoV-2 infection; SARS-CoV-2; Age Distribution; Antirheumatic Agents; Aspirin; C-Reactive Protein; COVID-19; Child; Child Preschool; Coronary Artery Disease; Cough; Diarrhea; Dyspnea; Female; Glucocorticoids; Heart Failure; Humans; Hyperferritinemia; Hypotension; Immunoglobulins Intravenous; Immunologic Factors; Infant; Intensive Care Units Pediatric; Interleukin 1 Receptor Antagonist Protein; Italy; Lymphopenia; Male; Mucocutaneous Lymph Node Syndrome; Myocarditis; Platelet Aggregation Inhibitors; SARS-CoV-2; Shock; Systemic Inflammatory Response Syndrome; Tachypnea; Troponin T; VomitingMalelcsh:Diseases of the musculoskeletal systemcoronary artery abnormalities; hypotension; kawasaki disease; multisystem inflammatory syndrome associated with coronavirus disease; myocarditis; pediatric inflammatory multisystem syndrome-temporally associated to SARS-CoV-2 infection; SARS-CoV-2; age distribution; antirheumatic agents; aspirin; C-reactive protein; COVID-19; child ; preschool; coronary artery disease; cough; diarrhea; yspnea; female; glucocorticoids; heart failure; humans; hyperferritinemia; hypotension; immunoglobulins; intravenous; immunologic factors; infant; intensive care units; pediatric; interleukin 1 receptor antagonist protein; italy; lymphopenia; male; mucocutaneous lymph node syndrome; myocarditis; platelet aggregation inhibitors; SARS-CoV-2; shock; systemic inflammatory response syndrome; tachypnea; troponin T; vomitingMyocarditiCoronary Artery Disease030204 cardiovascular system & hematologySARS-CoV-2 Kawasaki disease Pediatric inflammatory multisystem syndrome-temporally associated to SARS-CoV-2 infection Myocarditis Hypotension Multisystem inflammatory syndrome associated with coronavirus disease Coronary artery abnormalitiesCoronary artery diseaseSettore MED/38 - Pediatria Generale E Specialistica0302 clinical medicineGlucocorticoidImmunologic FactorMultisystem inflammatory syndrome associated with coronavirus diseaseImmunology and AllergyChildCoronary artery abnormalitieFisher's exact testPediatricTachypneabiologylcsh:RJ1-570Antirheumatic AgentImmunoglobulins IntravenousShockPediatric inflammatory multisystem syndrome-temporally associated to SARS-CoV-2 infectionSettore MED/38Systemic Inflammatory Response SyndromeIntensive Care UnitsMyocarditisC-Reactive ProteinItalyAntirheumatic AgentsChild PreschoolCohortsymbolsPlatelet aggregation inhibitorFemaleHypotensionIntravenousCoronary artery abnormalitiesHumanResearch ArticleDiarrheamedicine.medical_specialtyMyocarditisVomitingImmunoglobulinsMucocutaneous Lymph Node SyndromeIntensive Care Units Pediatric03 medical and health sciencessymbols.namesakeAge DistributionRheumatologyTroponin TInternal medicineLymphopeniamedicineHumansImmunologic FactorsPreschoolGlucocorticoids030203 arthritis & rheumatologyHeart FailureAspirinKawasaki diseasebusiness.industrySARS-CoV-2Platelet Aggregation InhibitorC-reactive proteinCOVID-19Infantlcsh:Pediatricsmedicine.diseaseSystemic inflammatory response syndromeInterleukin 1 Receptor Antagonist ProteinDyspneaCoughImmunoglobulins IntravenouPediatrics Perinatology and Child Healthbiology.proteinKawasaki diseaseHyperferritinemialcsh:RC925-935businessPlatelet Aggregation InhibitorsPediatric rheumatology online journal
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Intestinal Involvement in Kawasaki Disease

2018

Objectives To describe a case of Kawasaki disease with intestinal involvement and to analyze other published reports to define clinical characteristics, diagnostic issues, and therapeutic approaches of gastrointestinal involvement in Kawasaki disease. Study design A computerized search without language restriction was conducted using PubMed and SCOPUS. An article was considered eligible for inclusion in the systematic review if it reported data on patient(s) with intestinal involvement in Kawasaki disease. Our case was also included in the analysis. Results Thirty-three articles reporting 48 cases of Kawasaki disease with intestinal involvement were considered. Fever, abdominal pain, and vo…

Intestinal pseudo-obstructionMalemedicine.medical_specialtyPediatricsAbdominal painSettore MED/17 - Malattie InfettiveAdolescentFeverMucocutaneous Lymph Node SyndromeDiagnosis Differential03 medical and health sciences0302 clinical medicinepediatric gastroenterology030225 pediatricsmedicineintestinal pseudo-obstructionHumans030212 general & internal medicineHematologic TestPediatric gastroenterologyCoronary artery aneurysmGangreneAspirinHematologic TestsIntestinal Diseasebusiness.industryabdominal painImmunoglobulins Intravenousmedicine.diseasecoronary artery aneurysmHospitalizationIntestinal DiseasesImmunoglobulins IntravenouPediatrics Perinatology and Child HealthKawasakiSplenomegalyVomitingKawasaki diseasemedicine.symptombusinessTomography X-Ray ComputedBowel diseaseIntestinal Obstructionmedicine.drugHepatomegalyHuman
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BRAINSTEM AUDITORY EVOKED POTENTIALS AND VISUAL POTENTIALS IN KAWASAKI DISEASE: EXPRESSION OF CNS VASCULITIS?

2015

Kawasaki disease (KD) is an acute, self-limited vasculitis of infants and children that is nowadays the most common cause of acquired heart disease in children. Transient sensorineural hearing loss (20 to 35 dB) is a possible complication of acute phase KD and may be related to salicylate toxicity in some patients.

Kawasaki disease vasculitis heart disease
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Oral necrotizing microvasculitis in a patient affected by Kawasaki disease

2007

Kawasaki disease (KD) was first described in 1967 by Kawasaki, who defined it as ?mucocutaneous lymph node syndrome?. KD is an acute systemic vasculitis, which mainly involves medium calibre arteries; its origin is unknown, and it is observed in children under the age of 5, especially in their third year. The principal presentations of KD include fever, bilateral nonexudative conjunctivitis, erythema of the lips and oral mucosa, changes in the extremities, rash, and cervical lymphadenopathy. Within KD, oral mucositis ? represented by diffuse mucous membrane erythema, lip and tongue reddening and lingual papillae hypertrophy with subsequent development of strawberry tongue ? can occur both i…

Kawasaki diseaseORAL NECROTIZING MICROVASCULITISUNESCO::CIENCIAS MÉDICAS:CIENCIAS MÉDICAS [UNESCO]ORAL NECROTIZING MICROVASCULITIS;KAWASAKI DISEASEvasculitisKAWASAKI DISEASEoral mucositis
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